International Retinoblastoma Staging System

Notes

**Note 1:** This SSDI is effective for diagnosis years 2023+ * For cases diagnosed 2018-2022, leave this SSDI blank **Note 2:** Registrar is required to assign International Retinoblastoma Staging System (IRSS) based on the criteria provided in this data item. * If a physician documents the International Retinoblastoma Staging System (IRSS), document this in the text field, but don’t use that to code this data item **Note 3:** If there is bilateral disease, code the most advanced stage at diagnosis.

NAACCR Item

NAACCR #9612

Metadata

SSDI
Code Description
0 Stage 0: * Tumor confined to the globe * Enucleation has not been performed * Patient treated conservatively with either focal therapies or chemotherapy
1 Stage I: * Enucleation with negative margins (R0) - Completely resected histologically
2 Stage II * Enucleation with positive/microscopic residual tumor
3 Stage III: * Regional extension - Orbit - Preauricular extension - Cervical lymph node involvement
4 Stage IV: * Distant metastatic disease
8 Not applicable: Information not collected for this case (If this information is required by your standard setter, use of code 8 may result in an edit error.)
9 Not documented in medical record International Retinoblastoma Staging System (IRSS) not assessed or unknown if assessed
<BLANK> N/A - Diagnosis year is prior to 2023
(1) Aitken JF, Youlden D, O’Neill L, Gupta S, Frazier AL, eds. Childhood cancer staging for population registries according to the Toronto Childhood Cancer Stage Guidelines – Version 2. Cancer Council Queensland and Cancer Australia: Brisbane, Australia; 2021.