International Retinoblastoma Staging System
Notes
**Note 1:** This SSDI is effective for diagnosis years 2023+
* For cases diagnosed 2018-2022, leave this SSDI blank
**Note 2:** Registrar is required to assign International Retinoblastoma Staging System (IRSS) based on the criteria provided in this data item.
* If a physician documents the International Retinoblastoma Staging System (IRSS), document this in the text field, but don’t use that to code this data item
**Note 3:** If there is bilateral disease, code the most advanced stage at diagnosis.
Metadata
SSDI
| Code |
Description |
| 0 |
Stage 0:
* Tumor confined to the globe
* Enucleation has not been performed
* Patient treated conservatively with either focal therapies or chemotherapy |
| 1 |
Stage I:
* Enucleation with negative margins (R0)
- Completely resected histologically |
| 2 |
Stage II
* Enucleation with positive/microscopic residual tumor |
| 3 |
Stage III:
* Regional extension
- Orbit
- Preauricular extension
- Cervical lymph node involvement |
| 4 |
Stage IV:
* Distant metastatic disease |
| 8 |
Not applicable: Information not collected for this case
(If this information is required by your standard setter, use of code 8 may result in an edit error.) |
| 9 |
Not documented in medical record
International Retinoblastoma Staging System (IRSS) not assessed or unknown if assessed |
| <BLANK> |
N/A - Diagnosis year is prior to 2023 |
(1) Aitken JF, Youlden D, O’Neill L, Gupta S, Frazier AL, eds. Childhood cancer staging for population registries according to the Toronto Childhood Cancer Stage Guidelines – Version 2. Cancer Council Queensland and Cancer Australia: Brisbane, Australia; 2021.
