Pediatric Primary Tumor

This input is used in derivation

Notes

**Note 1:** : If there is bilateral disease, record the more advanced stage in Pediatric Primary Tumor. * Code the eye with the lesser stage in the data item IRSS Stage for Eye-2 [NAACCR Data item #9627]. **Note 2:** Pathological staging information from an enucleation always takes precedence over clinical staging, except in cases with neoadjuvant treatment where clinical disease is as extensive as or more extensive than disease at surgery.

Default

999

NAACCR Item

NAACCR #9623
Code Description
100 Intraocular tumor(s) WITHOUT any * Local invasion * Focal choroidal invasion * Pre- or intralaminar involvement of the optic nerve head Tumor confined to retina, NOS Localized, NOS
200 Intraocular tumor(s) WITH local invasion, NOS * Choroid (concomitant focal invasion) * Pre- or intralaminar involvement of optic nerve head * Retinal detachment * Schlemm's canal * Stromal invasion iris * Subretinal seeding * Trabecular meshwork * Vitreous seeding
300 Advanced intraocular tumor(s) WITH significant local invasion * Anterior chamber * Aseptic orbital cellulitis * Buphthalmos * Choroid (multiple foci, focal, full-thickness involvement) * Ciliary body * Emissary channels * Hyphema AND/OR massive vitreous hemorrhage * Iris * Lens * Pars plana * Phthisis or pre-phthisis bulbi * Raised intraocular pressure with neovascularization * Retrolaminar invasion of optic nerve head * Sclera * Zonules
400 Evidence of extraocular tumor * Tumor at transected end of optic nerve * Tumor in the meningeal spaces around optic nerve Full-thickness invasion of sclera WITH invasion of * Adjacent adipose tissue * Bone * Conjunctiva * Episcleral * Extraocular muscle * Eyelids
800 No evidence of primary tumor
999 Unknown; extension not stated Primary tumor cannot be assessed Not documented in medical record Death Certificate Only