| 0 |
Stage 0
* Tumor confined to the globe
* Enucleation has not been performed
* Patient treated conservatively with either focal therapies or chemotherapy |
| 1 |
Stage I
* Enucleation with negative margins (R0)
* Completely resected histologically |
| 2 |
Stage II
* Enucleation with positive/microscopic residual tumor |
| 3 |
Stage III
* Regional extension, involvement of
- Orbit
- Preauricular extension
- Cervical lymph node involvement |
| 4 |
Stage IV
* Distant metastatic disease |
| 7 |
Not applicable: Only one eye is involved and staging collected in Pediatric Primary Tumor, Pediatric Regional Nodes and Pediatric Mets |
| 8 |
Not applicable: Information not collected for this case
(If this information is required by your standard setter, use of code 8 may result in an edit error) |
| 9 |
Not documented in medical record
International Retinoblastoma Staging System (IRSS) not assessed or unknown if assessed |
| <BLANK> |
NA - Diagnosis year is prior to 2024 |
