Pediatric Primary Tumor

This input is used for staging

Wilms Tumor Staging System

Notes

**Note 1:** Primary tumor evaluation is based on a surgical resection of the primary site only. * Code 999 if there is no surgical resection of the primary site * Do not use imaging findings to code this data item **Note 2:** Codes are based on whether patient had neoadjuvant chemotherapy or surgery first * If patient did not receive chemotherapy (or unknown if patient received chemotherapy) prior to surgery, see codes 100, 200, 300 * If patient did receive chemotherapy prior to surgery, see codes 110, 210, 310 **Note 3:** If there is bilateral disease, code the most advanced stage at diagnosis. * Code 4 for Laterality [NAACCR # 410] data item

Default

999

NAACCR Item

NAACCR #9623
Code Description
100 No chemotherapy AND **no** biopsy prior to surgery (see code 300 if biopsy done prior to surgical resection) * Tumor limited to kidney and completely resected - Renal capsule intact, not penetrated by tumor - No tumor invasion of veins or lymphatics of renal sinus * Confined (limited) to the kidney, NOS * Localized, NOS * WITH NEGATIVE or UNKNOWN margins (see code 300 if positive margins)
110 Chemotherapy prior to surgery * Tumor limited to kidney and completely resected - Renal capsule may be infiltrated by tumor, but tumor does not reach the outer surface - Tumor may protrude or bulge into the pelvic system or ureter, but does not infiltrate - Vessels of renal sinus not involved
200 No chemotherapy and **no** biopsy prior to surgery (see code 300 if biopsy done prior to surgical resection) * Tumor extends beyond kidney but completely resected - Tumor penetrates renal capsule - Tumor in lymphatics or veins of renal sinus - Tumor in renal vein with margin not involved * WITH NEGATIVE or UNKNOWN margins (see code 300 if positive margins)
210 Chemotherapy prior to surgery * Tumor extends beyond kidney but completely resected - Tumor penetrates renal capsule into perirenal fat - Tumor infiltrates the renal sinus and/or invades blood and lymphatic vessels outside renal parenchyma but is completely resected - Tumor infiltrates adjacent organs or vena cava but is completely resected
300 No chemotherapy prior to surgery * Residual tumor confined to abdomen - Peritoneal contamination or tumor implant - Tumor spillage (rupture) of any degree occurring before or during surgery - Gross residual tumor in abdomen * WITH POSITIVE margins (includes localized tumor with positive margins) OR * Biopsy of tumor (including fine-needle aspiration) prior to surgical resection of kidney
310 Chemotherapy prior to surgery * Incomplete resection of the tumor (gross or microscopic extension beyond the resection margins) - Necrotic tumor or chemotherapy-induced changes - Tumor rupture before or intraoperatively - Tumor has penetrated the peritoneal surface - Tumor thrombi present at resection margins - Surgical biopsy prior to resection (does not include needle biopsy)
800 No evidence of primary tumor
999 Unknown; extension not stated Primary tumor cannot be assessed Not documented in medical record No surgical resection of the primary site Death certificate only
(1) Aitken JF, Youlden D, O’Neill L, Gupta S, Frazier AL, eds. Childhood cancer staging for population registries according to the Toronto Childhood Cancer Stage Guidelines – Version 2. Cancer Council Queensland and Cancer Australia: Brisbane, Australia; 2021.