Summary Stage 2018: Kaposi Sarcoma
Summary Stage 2018
Notes
**Kaposi Sarcoma**
9140 Kaposi Sarcoma (C000-C699, C739-C750, C754-C809)
**Note 1:** The following sources were used in the development of this chapter
* SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf)
* SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/)
* Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx
* Chapter 45 *Soft Tissue Sarcoma - Unusual Histologies and Sites*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois.
**Note 2:** Kaposi Sarcoma of the brain, central nervous system and intracranial glands is now collected in the following:
* C700, C710-C719: Brain
* C701, C709, C720-C725, C728-C729: CNS Other
* C751-C753: Intracranial Gland
**Note 3:** Summary Stage is the only applicable staging system for this site/histology/schema.
**Note 4:** Code 0 is not applicable for this chapter.
| SS2018 |
Description |
| 1 |
Localized only
- Single or multiple lesion(s)
+ Mucosa (e.g., oral cavity, anus, rectum, vagina, vulva)
+ Skin and/or connective tissue
+ Viscera (e.g., pulmonary, gastrointestinal tract, spleen, other) |
| 2 |
Regional by direct extension only
- Multiple lesion(s)
+ Mucosa plus skin and/or connective tissue
+ Viscera plus mucosa
+ Viscera plus skin and/or connective tissue |
| 3 |
Regional lymph node(s) involved only
- Both clinically enlarged palpable lymph node(s) (adenopathy) and pathologically positive lymph node(s)
- Clinically enlarged palpable lymph node(s) (adenopathy) and either pathologically negative node(s) or no pathological statement
- No clinically enlarged palpable lymph node(s) (adenopathy) but pathologically positive lymph node(s)
- Regional lymph node(s), NOS
+ Lymph node(s), NOS |
| 4 |
Regional by BOTH direct extension AND regional lymph node(s) involved
- Codes (2) + (3) |
| 7 |
Distant site(s)/lymph node(s) involved
- Distant site(s) (including further contiguous extension)
+ Multiple lesions in all THREE of following: viscera plus mucosa plus skin and/or connective tissue
- Distant lymph node(s), NOS
- Distant metastasis, NOS
+ Carcinomatosis
+ Distant metastasis WITH or WITHOUT distant lymph node(s) |
| 9 |
Unknown if extension or metastasis |
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998
(2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions,** National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001.
(3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05.** American Joint Committee on Cancer (Chicago, IL)
(4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017
(5) Pollock, R.E., Maki, R.G. **Introduction to Soft Tissue Sarcoma** In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017
(6) Maki, R.G., Pollock, R.E., et al. **Soft Tissue Sarcoma - Unusual Histologies and Sites**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al.
(Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 539-545
