CS Extension

Notes

**Note 1**: Ocular adnexal lymphomas (OAL) originate in conjunctiva, eyelids, lacrimal gland, lacrimal drainage apparatus, and other orbital tissues surrounding the eye. This schema should not be used for secondary lymphomatous involvement of ocular adnexa or for intraocular lymphomas. **Note 2**: Preseptal eyelid involvement includes infiltration of the outer three layers of the eyelid:skin, subcutaneous connective tissue, and orbicularis oculi muscle. **Note 3**: The orbit is the bony cavity containing the eye, lacrimal gland, lacrimal sac, nasolacrimal duct, extraocular muscles, fat. arteries, veins, and nerves, but no lymphatics. **Note 4**: Unknown extension is coded 989. Code 999, used for lymphoma staging in CS Version1, is an obsolete code for this schema.
Code Description AJCC 7 T AJCC 6 T Summary Stage 1977 T Summary Stage 2000 T
100 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of a single lymph node region
Stage I
ERROR: NA L L
105 Lymphoma involving bulbar conjunctiva only
WITHOUT orbital involvement

Stated as T1a with no other information on extension
T1a NA L L
110 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Localized involvement of a single extralymphatic organ/site in the absence of any lymph node involvement
Multifocal involvement of one extralymphatic organ/site
Stage IE
ERROR: NA L L
115 Palpebral conjunctiva
WITHOUT orbital involvement:
With or without involvement of the fornix
With or without involvement of the caruncle

Stated as T1b with no other information on extension
T1b NA L L
120 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of spleen only
Stage IS
ERROR: NA RNOS RNOS
125 Extensive conjunctival involvement

Stated as T1c with no other information on extension
T1c NA L L
150 Conjunctiva alone
WITHOUT orbital involvement,
Conjunctiva, NOS

Stated as T1[NOS] with no other information on extension
T1NOS NA L L
200 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of two or more lymph node regions on the SAME side of the diaphragm
Stage II
ERROR: NA RNOS RNOS
210 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Localized involvement of a single extralymphatic organ/site
WITH involvement of its regional lymph node(s) or
WITH or without involvement of other lymph node(s) on the SAME site of the diaphragm
Direct extension to adjacent organs or tissues
Stage IIE
ERROR: NA RNOS RNOS
220 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of spleen PLUS lymph node(s) BELOW the diaphragm
Stage IIS
ERROR: NA RNOS RNOS
230 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of spleen PLUS involvement of a single extralymphatic organ/site BELOW the diaphragm
WITH/WITHOUT involvement of lymph node(s) BELOW the diaphragm
Stage IIES
ERROR: NA RNOS RNOS
300 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of lymph node regions on BOTH sides of the diaphragm
Stage III
ERROR: NA D D
305 Anterior orbit
With or without conjunctival involvement

Stated as T2a with no other information on extension
T2a NA L L
310 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of an extralymphatic organ/site PLUS involvement of lymph node(s) on the OPPOSITE side of the diaphragm
Stage IIIE
ERROR: NA D D
315 Anterior orbit
WITH lacrimal involvement:
With or without conjunctival involvement

Stated as T2b with no other information on extension
T2b NA L L
320 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Involvement of the spleen PLUS lymph node(s) ABOVE the diaphragm
Involvement of spleen PLUS lymph nodes on both sides of the diaphragm
Stage IIIS
ERROR: NA D D
325 Posterior orbit:
With or without conjunctival involvement
With or without anterior involvement
With or without extraocular muscle involvement

Stated as T2c with no other information on extension
T2c NA L L
330 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

(310 + 320) OR
Involvement of the spleen PLUS a single extralymphatic site ABOVE the diaphragm
WITH/WITHOUT involvement of lymph node(s)
Involvement of the spleen PLUS involvement of lymph node region(s) ABOVE the diaphragm
PLUS involvement of a single extralymphatic organ/site on either side of the diaphragm
Stage IIIES
ERROR: NA D D
335 Nasolacrimal drainage system:
With or without conjunctival involvement
Without nasopharynx involvement

Stated as T2d with no other information on extension
T2d NA L L
350 Orbital involvement:
With or without conjunctival involvement

Stated as T2 [NOS] with no other information on extension
T2NOS NA L L
500 Pre-septal eyelid involvement:
With or without orbital involvement
With or without conjunctival involvement

Stated as T3 with no other information on extension
T3 NA L L
700 Nasopharynx

Stated as T4a with no other information on extension
T4a NA D D
710 Osseous involvement including periosteum

Stated as T4b with no other information on extension
T4b NA D D
720 Maxillofacial, ethmoidal, and/or frontal sinuses

Stated as T4c with no other information on extension
T4c NA D D
730 Intracranial spread

Stated as T4d with no other information on extension
T4d NA D D
750 Extension beyond orbit to adjacent structures, NOS

Stated as T4 [NOS] with no other information on extension
T4NOS NA D D
800 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Diffuse or disseminated (multifocal) involvement of ONE OR MORE extralymphatic organ(s)/site(s)
WITH OR WITHOUT associated lymph node involvement
Multifocal involvement of MORE THAN ONE extralymphatic organ/site
Involvement of isolated extralymphatic organ in absence of involvement of adjacent lymph nodes, but in conjunction with disease in distant sites
Metastasis/involvement:
Bone marrow
Liver
Nodular involvement of lung(s)
Stage IV
ERROR: NA D D
805 Further contiguous extension beyond any structure in codes 700 - 730 T4NOS NA D D
950 No evidence of primary tumor T0 NA U U
989 Unknown; extension not stated
Primary tumor cannot be assessed
Not documented in patient record
TX NA U U
999 OBSOLETE DATA RETAINED V0200
New schema for site/histology V0200

Unknown extension
Primary tumor cannot be assessed
Not documented in patient record
ERROR: NA U U
- Stage grouping for AJCC 6 staging of ocular adnexal lymphoma for cases using obsolete codes is derived directly from the CS Extension code as shown in the AJCC TNM 6 Stage CSv1 table. A or B classification is appended to Stage I-IV based on coding of CS Site-Specific Factor 2, Systemic Symptoms at Diagnosis. - Stage grouping for AJCC 6 staging of ocular adnexal lymphoma is derived from a combination of CS Extension, CS Lymph Nodes, and CS Mets at DX codes as shown in the AJCC TNM 6 Stage table. A or B classification is appended to Stage I-IV based on coding of CS Site-Specific Factor 2, Systemic Symptoms at Diagnosis.