Retinoblastoma

Primary Site Histology Staging Type
C690-C691, C693-C696, C698-C699 9510-9514 Summary Stage only
C692 9510-9514 TNM 7 and Summary Stage

If you are working with a site/histology that only summary stages and you need to directly code it, please use the SEER Summary Stage 2000 manual

Notes

C690 Conjunctiva
C691 Cornea, NOS
C692 Retina
C693 Choroid
C694 Ciliary Body
C695 Lacrimal Gland
C696 Orbit, NOS
C698 Overlapping lesion of eye and adnexa
C699 Eye, NOS

Note 1: This schema is based on the UICC chapter Retinoblastoma, pages 291-297.

  • Primary sites C690, C691, C693-C696, C698, and C699 are not listed in this chapter of the UICC manual; however, they are included in this schema
  • Only retinoblastomas with primary site C692 will be TNM staged
  • TNM is defined for this site; however, there is no stage group

Note 2: Laterality must be coded for this site. In bilateral cases, the eyes should be classified separately.

Note 3: This classification does not apply to complete spontaneous regression of the tumor.

Note 4: In addition to directly assigning TNM, Summary Stage 2000 (SS2000) must be captured. If directly assigning SS2000, use the Retinoblastoma chapter on page 264 of the SS2000 on-line manual.

Main Data Items

Name Default Value Used for Staging NAACCR Item Required By Metadata
Clinical T <BLANK> Yes NAACCR #940 None
Clinical N <BLANK> Yes NAACCR #950 None
Clinical M <BLANK> Yes NAACCR #960 None
TNM Clin Stage Group 88 Yes NAACCR #970 None
Pathologic T <BLANK> Yes NAACCR #880 None
Pathologic N <BLANK> Yes NAACCR #890 None
Pathologic M <BLANK> Yes NAACCR #900 None
TNM Path Stage Group 88 Yes NAACCR #910 None
SSF2: Retinoblastoma (RB) Gene Mutation 988 No NAACCR #2890 None None
SSF3: Family History of Retinoblastoma 988 No NAACCR #2900 None None
SSF4: Primary Globe-Sparing Treatment Failure 988 No NAACCR #2910 None None
SSF5: Linear Choroidal Invasion 988 No NAACCR #2920 None None
SSF6: Clinical Extension for Second Eye 988 No NAACCR #2930 None None

Additional Data Items

Name Default Value Used for Staging NAACCR Item Required By Metadata
Year of Diagnosis <BLANK> No NAACCR #390 None
Primary Site <BLANK> Yes NAACCR #400 None
Histology <BLANK> Yes NAACCR #522 None
RX Summ Systemic/Surgery Sequence <BLANK> Yes NAACCR #1639 None
RX Summ Surgery/Radiation Sequence <BLANK> Yes NAACCR #1380 None
Regional Nodes Positive <BLANK> Yes NAACCR #820 None