Retinoblastoma
Primary Site | Histology | Staging Type |
---|---|---|
C690-C691, C693-C696, C698-C699 | 9510-9514 | Summary Stage only |
C692 | 9510-9514 | TNM 7 and Summary Stage |
If you are working with a site/histology that only summary stages and you need to directly code it, please use the SEER Summary Stage 2000 manual
Notes
C690 Conjunctiva
C691 Cornea, NOS
C692 Retina
C693 Choroid
C694 Ciliary Body
C695 Lacrimal Gland
C696 Orbit, NOS
C698 Overlapping lesion of eye and adnexa
C699 Eye, NOS
Note 1: This schema is based on the UICC chapter Retinoblastoma, pages 291-297.
- Primary sites C690, C691, C693-C696, C698, and C699 are not listed in this chapter of the UICC manual; however, they are included in this schema
- Only retinoblastomas with primary site C692 will be TNM staged
- TNM is defined for this site; however, there is no stage group
Note 2: Laterality must be coded for this site. In bilateral cases, the eyes should be classified separately.
Note 3: This classification does not apply to complete spontaneous regression of the tumor.
Note 4: In addition to directly assigning TNM, Summary Stage 2000 (SS2000) must be captured. If directly assigning SS2000, use the Retinoblastoma chapter on page 264 of the SS2000 on-line manual.
Main Data Items
Name | Default Value | Used for Staging | NAACCR Item | Required By | Metadata |
---|---|---|---|---|---|
Clinical T | <BLANK> | Yes | NAACCR #940 | None | |
Clinical N | <BLANK> | Yes | NAACCR #950 | None | |
Clinical M | <BLANK> | Yes | NAACCR #960 | None | |
TNM Clin Stage Group | 88 | Yes | NAACCR #970 | None | |
Pathologic T | <BLANK> | Yes | NAACCR #880 | None | |
Pathologic N | <BLANK> | Yes | NAACCR #890 | None | |
Pathologic M | <BLANK> | Yes | NAACCR #900 | None | |
TNM Path Stage Group | 88 | Yes | NAACCR #910 | None | |
SSF2: Retinoblastoma (RB) Gene Mutation | 988 | No | NAACCR #2890 | None | None |
SSF3: Family History of Retinoblastoma | 988 | No | NAACCR #2900 | None | None |
SSF4: Primary Globe-Sparing Treatment Failure | 988 | No | NAACCR #2910 | None | None |
SSF5: Linear Choroidal Invasion | 988 | No | NAACCR #2920 | None | None |
SSF6: Clinical Extension for Second Eye | 988 | No | NAACCR #2930 | None | None |
Additional Data Items
Name | Default Value | Used for Staging | NAACCR Item | Required By | Metadata |
---|---|---|---|---|---|
Year of Diagnosis | <BLANK> | No | NAACCR #390 | None | |
Primary Site | <BLANK> | Yes | NAACCR #400 | None | |
Histology | <BLANK> | Yes | NAACCR #522 | None | |
RX Summ Systemic/Surgery Sequence | <BLANK> | Yes | NAACCR #1639 | None | |
RX Summ Surgery/Radiation Sequence | <BLANK> | Yes | NAACCR #1380 | None | |
Regional Nodes Positive | <BLANK> | Yes | NAACCR #820 | None |