Retinoblastoma

Primary Site Histology Staging Type
C690-C691, C693-C696, C698-C699 9510-9514 Summary Stage only
C692 9510-9514 TNM 7 and Summary Stage

If you are working with a site/histology that only summary stages and you need to directly code it, please use the SEER Summary Stage 2000 manual

Notes

C690 Conjunctiva C691 Cornea, NOS C692 Retina C693 Choroid C694 Ciliary Body C695 Lacrimal Gland C696 Orbit, NOS C698 Overlapping lesion of eye and adnexa C699 Eye, NOS **Note 1:** This schema is based on the UICC chapter *Retinoblastoma,* pages 291-297. * Primary sites C690, C691, C693-C696, C698, and C699 are not listed in this chapter of the UICC manual; however, they are included in this schema * Only retinoblastomas with primary site C692 will be TNM staged * TNM is defined for this site; however, there is no stage group **Note 2:** Laterality must be coded for this site. In bilateral cases, the eyes should be classified separately. **Note 3:** This classification does not apply to complete spontaneous regression of the tumor. **Note 4:** In addition to directly assigning TNM, Summary Stage 2000 (SS2000) must be captured. If directly assigning SS2000, use the *Retinoblastoma* chapter on page 264 of the [SS2000 on-line manual](http://seer.cancer.gov/tools/ssm/SSSM2000-122012.pdf#page=264).

Main Data Items

Name Default Value Used for Staging NAACCR Item Required By Metadata
Clinical T <BLANK> Yes NAACCR #940 None
Clinical N <BLANK> Yes NAACCR #950 None
Clinical M <BLANK> Yes NAACCR #960 None
TNM Clin Stage Group 88 Yes NAACCR #970 None
Pathologic T <BLANK> Yes NAACCR #880 None
Pathologic N <BLANK> Yes NAACCR #890 None
Pathologic M <BLANK> Yes NAACCR #900 None
TNM Path Stage Group 88 Yes NAACCR #910 None
SSF2: Retinoblastoma (RB) Gene Mutation 988 No NAACCR #2890 None None
SSF3: Family History of Retinoblastoma 988 No NAACCR #2900 None None
SSF4: Primary Globe-Sparing Treatment Failure 988 No NAACCR #2910 None None
SSF5: Linear Choroidal Invasion 988 No NAACCR #2920 None None
SSF6: Clinical Extension for Second Eye 988 No NAACCR #2930 None None

Additional Data Items

Name Default Value Used for Staging NAACCR Item Required By Metadata
Year of Diagnosis <BLANK> No NAACCR #390 None
Primary Site <BLANK> Yes NAACCR #400 None
Histology <BLANK> Yes NAACCR #522 None
RX Summ Systemic/Surgery Sequence <BLANK> Yes NAACCR #1639 None
RX Summ Surgery/Radiation Sequence <BLANK> Yes NAACCR #1380 None
Regional Nodes Positive <BLANK> Yes NAACCR #820 None

Initial Context

Staging Methods

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TNM 7 Stage

Inclusion Table

Primary Site Histology
C692 9510-9514

Start

Additional Context
Pathologic Stage Group = 90
Clinical Stage Group = 90

Next Step

  2. Parse T
  3. clin_t_prefix
    tmp_clin_t

Next Step

  2. Parse N
  3. clin_n_prefix
    tmp_clin_n

Next Step

  2. Parse M
  3. tmp_clin_m
    clin_m_prefix

Next Step

  2. Parse T
  3. tmp_path_t
    path_t_prefix

Next Step

  2. Parse N
  3. tmp_path_n
    path_n_prefix

Next Step

  2. Parse M
  3. tmp_path_m
    path_m_prefix

Next Step

  2. Determine Default T
  3. Source T
    tmp_path_t
    tmp_clin_t
    tmp_combined_t

Next Step

  2. Determine Default N
  3. tmp_combined_n
    tmp_clin_n
    tmp_path_n
    Source N

Next Step

  2. Determine Default M
  3. tmp_path_m
    tmp_combined_m
    tmp_clin_m
    Source M

Next Step

  2. TNM 7 Stage Group
  3. Clinical Stage Group

Next Step

  2. TNM 7 Stage Group
  3. Pathologic Stage Group

Next Step

  2. Adjust Path Defaults for No Clin, No Path, Stage Group not defined
  3. tmp_combined_n
    tmp_combined_m
    Source T
    Clinical Stage Group
    Pathologic Stage Group
    Source N
    tmp_combined_t
    Source M

End

Combined Stage

Inclusion Table

Primary Site Histology
C692 9510-9514

Start

Additional Context
Combined Stage Group = 90
Combined N = 90
Combined M = 90
Combined T = 90

Next Step

  2. Stop if No Clin and No Path
  3. Combined M
    Combined N
    Source T
    tmp_continue
    Combined T
    Combined Stage Group
    Source N
    ss2017
    Source M

Next Step

  2. Combined T Retinoblastoma
  3. Source T
    tmp_combined_t

Next Step

  2. Combined N
  3. tmp_combined_n
    Source N

Next Step

  2. Combined M
  3. tmp_combined_m
    tmp_source_m
    Source M

Next Step

  2. Determine Combined Prefix
  3. cmb_t_prefix

Next Step

  2. Determine Combined Prefix
  3. cmb_n_prefix

Next Step

  2. Determine Combined Prefix
  3. cmb_m_prefix

Next Step

  2. Concatenate T
  3. Combined T

Next Step

  2. Concatenate N
  3. Combined N

Next Step

  2. Concatenate M
  3. Combined M

Next Step

  2. TNM 7 Stage Group
  3. Combined Stage Group

End

Outputs

Name Default Value Description NAACCR Item Metadata
Derived Version 1.2 None None
Derived SEER Clin Stage Group 88 NAACCR #3610
None 		None
Derived SEER Path Stage Group 88 NAACCR #3605
None 		None
Derived SEER Combined Stage Group 88 NAACCR #3614
None 		None
Derived SEER Combined T 88 NAACCR #3616
None 		None
Derived SEER Combined N 88 NAACCR #3618
None 		None
Derived SEER Combined M 88 NAACCR #3620
None 		None
Derived SEER Combined T Source <BLANK> NAACCR #3622
None 		None
Derived SEER Combined N Source <BLANK> NAACCR #3624
None 		None
Derived SEER Combined M Source <BLANK> NAACCR #3626
None 		None