Pediatric Primary Tumor
This input is used in derivation
Notes
**Note 1:** If there are bilateral retinoblastomas (both eyes involved), record the stage of the eye with the **more advanced/higher stage** in this data item. * Code the eye with the **lesser/lower stage** in the data item IRSS Stage for Eye-2 [NAACCR Data Item #1188] **Note 2:** Pathological staging information from an enucleation always takes precedence over clinical staging, except in cases with neoadjuvant treatment where clinical disease is as extensive as or more extensive than disease at surgery.Default
999NAACCR Item
NAACCR #1136| Code | Description |
|---|---|
| 100 | Intraocular tumor(s) WITHOUT any * Local invasion * Focal choroidal invasion * Pre- or intralaminar involvement of the optic nerve head Tumor confined to retina, NOS Localized, NOS |
| 200 | Intraocular tumor(s) WITH local invasion, NOS * Choroid (concomitant focal invasion) * Pre- or intralaminar involvement of optic nerve head * Retinal detachment * Schlemm's canal * Stromal invasion iris * Subretinal seeding * Trabecular meshwork * Vitreous seeding |
| 300 | Advanced intraocular tumor(s) WITH significant local invasion * Anterior chamber * Aseptic orbital cellulitis * Buphthalmos * Choroid (multiple foci, focal, full-thickness involvement) * Ciliary body * Emissary channels * Hyphema AND/OR massive vitreous hemorrhage * Iris * Lens * Pars plana * Phthisis or pre-phthisis bulbi * Raised intraocular pressure with neovascularization * Retrolaminar invasion of optic nerve head * Sclera * Zonules |
| 400 | Evidence of extraocular tumor * Tumor at transected end of optic nerve * Tumor in the meningeal spaces around optic nerve Full-thickness invasion of sclera WITH invasion of * Adjacent adipose tissue * Bone * Conjunctiva * Episcleral * Extraocular muscle * Eyelids |
| 800 | No evidence of primary tumor |
| 999 | Unknown; extension not stated Primary tumor cannot be assessed Not documented in medical record Death Certificate Only |