EOD Primary Tumor

Notes

**Note:** This is a new schema for pheochromocytomas (PHs) and paragangliomas (PGs), which are rare neuroendocrine tumors originating in the paraganglia. Pheochromocytomas originate in the adrenal medulla and sympathetic tumors. Paragangliomas originate either in the parasympathetic or sympathetic autonomous nervous system ganglia, which is outside the adrenal medulla.
Code Description SS2018 T
000 In situ: Noninvasive; intraepithelial IS
100 Any size pheochromocytoma (PH) tumor, no extra-adrenal invasion (8700/3) Confined to adrenal gland Localized, NOS L
200 Any size paraganglioma (PG) tumor, no extra-adrenal invasion (8680/3, 8690/3, 8692/3-8693/3) L
300 Adjacent connective tissue Gerota's fascia Invasion of adjacent organs - Blood vessels (large) + Renal vein + Vena cava - Kidney - Retroperitoneal structures including + Great vessels * Aorta * Inferior vena cava RE
700 Diaphragm Liver Pancreas Spleen Further contiguous extension D
800 No evidence of primary tumor U
999 Unknown; extension not stated Primary tumor cannot be assessed Not documented in medical record Death Certificate Only U
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