EOD Primary Tumor
Notes
**Note:** This is a new schema for pheochromocytomas (PHs) and paragangliomas (PGs), which are rare neuroendocrine tumors originating in the paraganglia. Pheochromocytomas originate in the adrenal medulla and sympathetic tumors. Paragangliomas originate either in the parasympathetic or sympathetic autonomous nervous system ganglia, which is outside the adrenal medulla.
Code |
Description |
SS2018 T |
000 |
In situ: Noninvasive; intraepithelial |
IS |
100 |
Any size pheochromocytoma (PH) tumor, no extra-adrenal invasion
Confined to adrenal gland
Localized, NOS |
L |
200 |
Any size paraganglioma (PG) tumor, no extra-adrenal invasion |
L |
300 |
Adjacent connective tissue
Gerota’s fascia
Invasion of adjacent organs
- Blood vessels (large)
+ Renal vein
+ Vena cava
- Kidney
- Retroperitoneal structures including
+ Great vessels
* Aorta
* Inferior vena cava |
RE |
700 |
Diaphragm
Liver
Pancreas
Spleen
Further contiguous extension |
D |
800 |
No evidence of primary tumor |
U |
999 |
Unknown; extension not stated
Primary tumor cannot be assessed
Not documented in patient record
Death Certificate Only |
U |
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