Lymphoma Ocular Adnexa

Primary Site Histology
C441, C690, C695-C696 9590-9699, 9702-9719, 9725-9726, 9734-9738, 9823, 9826-9827, 9930

Notes

9590-9699, 9702-9719, 9725-9726, 9734-9738, 9823, 9826-9827, 9930 (C441, C690, C695-C696) **Note 1:** **Sources used in the development of this schema** * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 71 *Ocular Adnexal Lymphoma*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** **Origination of Ocular Adnexal Lymphomas** * Ocular adnexal lymphomas (OAL) originate in conjunctiva, eyelids, lacrimal gland, lacrimal drainage apparatus, and other orbital tissues surrounding the eye. This schema should not be used for secondary lymphomatous involvement of ocular adnexa or for intraocular lymphomas. **Note 3:** **The preferred histology terms in this schema are based on the 2024 WHO Classification of Tumours, Haematolymphoid Tumours, 5th edition.** * 9590: Malignant lymphoma, NOS * 9591: Malignant lymphoma, non-Hodgkin, NOS * 9596: Mediastinal grey zone lymphoma (MGZL) * 9597: Primary cutaneous follicle centre lymphoma (PCFCL) * 9650: Classic Hodgkin lymphoma (CHL), NOS * 9651: Classic Hodgkin lymphoma, lymphocyte-rich (LR-cHL) * 9652: Classic Hodgkin lymphoma, mixed cellularity (MC-cHL) * 9653: Classic Hodgkin lymphoma, lymphocyte-depleted, NOS (LD-cHL) * 9659: Nodular lymphocyte predominant Hodgkin lymphoma (NLPHL) * 9663: Classic Hodgkin lymphoma, nodular sclerosis, NOS (NSCHL) * 9673: Mantle cell lymphoma (MCL) * 9678: Primary effusion lymphoma (PEL) * 9679: Primary mediastinal large B-cell lymphoma (PBML/PMBCL) * 9680: Diffuse large B-cell lymphoma (DLBCL) * 9687: Burkitt lymphoma (BL), NOS * 9688: T-cell/histiocyte-rich large B-cell lymphoma (THRLBCL) * 9689: Splenic marginal zone lymphoma (SMZL) * 9690 Follicular lymphoma (FL), NOS (except C700-C729, C751-C753 for 1/1/2023+) * 9691: Follicular lymphoma, grade 2 * 9695: Follicular lymphoma, grade 1 * 9698: Follicular lymphoma, grade 3 * 9699: Extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue (MALT lymphoma) * 9702: Peripheral T-cell lymphoma, NOS * 9705: Nodal T follicular helper cell lymphoma, angioimmunoblastic type * 9708: Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) * 9709: Primary cutaneous peripheral T-cell lymphomas (pcCTCL) * 9712: Intravascular large B-cell lymphoma (IVLBCL) * 9714: Anaplastic large cell lymphoma, ALK-positive (ALCL) * 9715: Anaplastic large cell lymphoma, ALK-negative (ALK-ALCL) (2021+ only) * 9716: Hepatosplenic T-cell lymphoma (HSTCL) * 9717: Intestinal T-cell lymphoma, NOS (ITCL-NOS) * 9718: Primary cutaneous anaplastic large cell lymphoma (C-ALCL) * 9719: Extranodal NK/T-cell lymphoma (ENKTL) (except C700-C729, C751-C753 for 1/1/2023+) * 9725: Hydroa vacciniforme-like lymphoma (2018-2020 only, nonreportable as of 2021) * 9726 Primary cutaneous gamma-delta T-cell lymphoma (PCGD-TCL) (2018-2020 only, see code 9687/3 for 2021+) * 9734: Extramedullary plasmacytoma (EMP) * 9735: Plasmablastic lymphoma (PBL) * 9737: ALK-positive large B-cell lymphoma (ALK+LBCL) * 9738: KSHV/HHV8-positive diffuse large B-cell lymphoma * 9823: Chronic lymphocytic leukemia/small lymphocytic lymphoma (CLL/SLL) * 9826: Burkitt cell leukemia (2018-2020 only, see code 9687/3 for 2021+) * 9827: Adult T-cell leukemia/lymphoma (ATLL) * 9930: Myeloid Sarcoma

Data Items

Name Default Value Used in Derivation NAACCR Item Required By Metadata
Year of Diagnosis No NAACCR #390
dateOfDiagnosis
None
Primary Site Yes NAACCR #400
primarySite
None
Histology Yes NAACCR #522
histologicTypeIcdO3
None
Type of Reporting Source No NAACCR #500
typeOfReportingSource
None
Tumor Size Clinical No NAACCR #752
tumorSizeClinical
None
Tumor Size Pathological No NAACCR #754
tumorSizePathologic
None
Tumor Size Summary 999 No NAACCR #756
tumorSizeSummary
None
Regional Nodes Positive 99 No NAACCR #820
regionalNodesPositive
None
Regional Nodes Examined 99 No NAACCR #830
regionalNodesExamined
None
Neoadjuvant Therapy 9 No NAACCR #1632
neoadjuvantTherapy
None
Neoadjuvant Therapy – Clinical Response 9 No NAACCR #1633
neoadjuvTherapyClinicalResponse
None
Neoadjuvant Therapy – Treatment Effect 9 No NAACCR #1634
neoadjuvTherapyTreatmentEffect
None
EOD Primary Tumor 999 Yes NAACCR #772
eodPrimaryTumor
None
EOD Regional Nodes 999 Yes NAACCR #774
eodRegionalNodes
None
EOD Mets 00 Yes NAACCR #776
eodMets
None
SS2018 No NAACCR #764
summaryStage2018
None
Grade Clinical 9 Yes NAACCR #3843
gradeClinical
All SSDI
Grade Pathological 9 Yes NAACCR #3844
gradePathological
All SSDI
Grade Post Therapy Clin (yc) No NAACCR #1068
gradePostTherapyClin
COC
NPCR
SEER
SSDI
Grade Post Therapy Path (yp) No NAACCR #3845
gradePostTherapy
CCCR/Canada
COC
NPCR
SEER
SSDI

Initial Context

Staging Methods

Expand All | Collapse All

Summary Stage 2018

Start

  1. Derived Summary Grade
  2. derived_summary_grade

Next Step

  1. EOD Primary Tumor
  2. ss2018_t

Next Step

  1. EOD Regional Nodes
  2. ss2018_n

Next Step

  1. EOD Mets
  2. ss2018_m

Next Step

  1. Summary Stage
  2. ss2018_derived

End

Outputs

Name Default Value Description NAACCR Item Metadata
Schema ID 00710 NAACCR #3800
schemaId
None
Derived Version {{ctx_alg_version}} None None
Derived Summary Stage 2018 9 NAACCR #762
derivedSummaryStage2018
None
Derived Summary Grade 2018 <BLANK> NAACCR #1975
derivedSummaryGrade2018
None