Retinoblastoma
| Primary Site | Histology | 
|---|---|
| C690-C696, C698-C699 | 9510-9514 | 
Notes
9510-9514 C690 Conjunctiva C691 Cornea, NOS C692 Retina C693 Choroid C694 Ciliary Body C695 Lacrimal Gland C696 Orbit, NOS C698 Overlapping lesion of eye and adnexa C699 Eye, NOS **Note:** The following sources were used in the development of this schema * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 68 *Retinoblastoma*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois.Data Items
| Name | Default Value | Used in Derivation | NAACCR Item | Required By | Metadata | 
|---|---|---|---|---|---|
| Year of Diagnosis | No | 
                    NAACCR #390
                    
                         dateOfDiagnosis  | 
            
            
                None | ||
| Primary Site | Yes | 
                    NAACCR #400
                    
                         primarySite  | 
            
            
                None | ||
| Histology | Yes | 
                    NAACCR #522
                    
                         histologicTypeIcdO3  | 
            
            
                None | ||
| Tumor Size Clinical | No | 
                    NAACCR #752
                    
                         tumorSizeClinical  | 
            
            
                None | ||
| Tumor Size Pathological | No | 
                    NAACCR #754
                    
                         tumorSizePathologic  | 
            
            
                None | ||
| Tumor Size Summary | 999 | No | 
                    NAACCR #756
                    
                         tumorSizeSummary  | 
            
            
                None | |
| Regional Nodes Positive | 99 | No | 
                    NAACCR #820
                    
                         regionalNodesPositive  | 
            
            
                None | |
| Regional Nodes Examined | 99 | No | 
                    NAACCR #830
                    
                         regionalNodesExamined  | 
            
            
                None | |
| LVI | 8 | No | 
                    NAACCR #1182
                    
                         lymphVascularInvasion  | 
            
            
                None | |
| RX Summ Surgery/Radiation Sequence | No | 
                    NAACCR #1380
                    
                         rxSummSurgRadSeq  | 
            
            
                None | ||
| RX Summ Systemic/Surgery Sequence | No | 
                    NAACCR #1639
                    
                         rxSummSystemicSurSeq  | 
            
            
                None | ||
| EOD Primary Tumor | 999 | Yes | 
                    NAACCR #772
                    
                         eodPrimaryTumor  | 
            
            
                None | |
| EOD Regional Nodes | 999 | Yes | 
                    NAACCR #774
                    
                         eodRegionalNodes  | 
            
            
                None | |
| EOD Mets | 00 | Yes | 
                    NAACCR #776
                    
                         eodMets  | 
            
            
                None | |
| SS2018 | No | 
                    NAACCR #764
                    
                         summaryStage2018  | 
            
            
                None | ||
| Grade Clinical | 9 | No | 
                    NAACCR #3843
                    
                         gradeClinical  | 
            
            
                CCCR/Canada COC NPCR SEER  | 
            
            SSDI | 
| Grade Pathological | 9 | No | 
                    NAACCR #3844
                    
                         gradePathological  | 
            
            
                CCCR/Canada COC NPCR SEER  | 
            
            SSDI | 
| Grade Post Therapy Clin (yc) | No | 
                    NAACCR #1068
                    
                         gradePostTherapyClin  | 
            
            
                COC NPCR SEER  | 
            
            SSDI | |
| Grade Post Therapy Path (yp) | No | 
                    NAACCR #3845
                    
                         gradePostTherapy  | 
            
            
                CCCR/Canada COC NPCR SEER  | 
            
            SSDI | |
| Heritable Trait | 9 | No | 
                    NAACCR #3856
                    
                         heritableTrait  | 
            
            
                CCCR/Canada COC SEER  | 
            
            SSDI | 
Initial Context
Outputs
| Name | Default Value | Description | NAACCR Item | Metadata | 
|---|---|---|---|---|
| Schema ID | 00680 | 
                    NAACCR #3800
                    
                         schemaId  | 
            
            None | |
| Derived Version | {{ctx_alg_version}} | None | None | |
| Derived Summary Stage 2018 | 9 | 
                    NAACCR #762
                    
                         derivedSummaryStage2018  | 
            
            None |