Lymphoma
| Primary Site | Histology | Behavior | Schema Discriminator 1 | 
|---|---|---|---|
| C000-C424, C470-C509, C511-C608, C619-C631, C637-C689, C691-C694, C698-C699, C739-C749, C760-C809 | 9590, 9596-9663, 9673-9699, 9702-9719, 9725-9726, 9735, 9737-9738 | <Any value> | |
| C440, C442-C449, C510, C609, C632 | 9590, 9596, 9650-9663, 9673-9679, 9687-9699, 9702-9705, 9714-9717, 9725, 9735, 9737-9738 | <Any value> | |
| C700-C729, C751-C753 | 9590, 9596-9663, 9673-9679, 9687-9698, 9716-9719, 9725-9726, 9735, 9737-9738 | 3 | |
| C750, C754-C759 | 9590, 9596-9663, 9673-9699, 9702-9719, 9725-9726, 9735, 9737-9738 | <Any value> | <Any value> | 
| C000-C440, C442-C689, C691-C694, C698-C699, C739-C749, C750, C754-C759, C760-C809 | 9591 | <Any value> | 3, 9 | 
| C700-C729, C751-C753 | 9591 | 3 | 3, 9 | 
| C000-C440, C442-C689, C691-C694, C698-C699, C739-C749, C750, C754-C759, C760-C809 | 9826-9827 | <Any value> | <Any value> | 
| C700-C729, C751-C753 | 9826-9827 | 3 | <Any value> | 
Notes
9590, 9596-9663, 9673-9699, 9702-9719, 9725-9726, 9735, 9737-9738, 9826-9827 (varying primary sites and histologies) * *See SSDI Manual, Appendix A: Schema ID 00790: Lymphoma for detailed listing of primary site/histology combinations for this schema* 9591 and Schema Discriminator 1: 3, 9 (C000-C440, C442-C689, C691-C694, C698-C809) **Note 1:** The following sources were used in the development of this schema * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 79 *Hodgkin and Non-Hodgkin Lymphomas*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. * Chapter 80 *Pediatric Hodgkin and Non-Hodgkin Lymphomas*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** See the following schemas for the listed histologies * C000-C440, C442-C689, C691-C694, C698-C809 (9823): *Lymphoma-CLL/SLL* * C441, C690, C695-C696 (9590-9699, 9673-9699, 9702-9719, 9725-9726, 9734-9738, 9823, 9826-9827, 9930): *Lymphoma Ocular Adnexa* * C440, C442-C449, C510, C609, C632 (9597, 9680, 9708-9709, 9712, 9718-9719, 9726): *Primary Cutaneous Lymphomas* * C700, C710-C719 (9680, 9699, 9702-9715): *Brain* * C701, C709, C720-C725, C728-C729 (9680, 9699, 9702-9715): *CNS Other* * C751-C753 (9680, 9699, 9702-9715): *Intracranial Gland* * 9591 and Schema Discriminator 1: 1, 2 (C000-C440, C442-C689, C691-C694, C698-C809): *HemeRetic* **Note 3:** The Cotswold modification of the Ann Arbor staging system (used in AJCC 6th and 7th editions) has been updated to the *Lugano classification*. The *Lugano classification* includes an E suffix for lymphoma with either localized extralymphatic presentations (Stage IE) or by contiguous spread from nodal disease (Stage IIE). A change from the Cotswold modification of the Ann Arbor Staging System, E lesions do not apply to patients with Stage III nodal disease; or any patient with nodal disease above and below the diaphragm with concurrent contiguous extralymphatic involvement (Stage IV), which was previously Stage IIIE. **Note 4:** Schema includes the preferred terms based on the *2017 WHO Classification of Haematopoietic and Lymphoid Tissues* 9590 Malignant lymphoma, NOS 9591 Non-Hodgkin lymphoma, NOS 9596 B-cell lymphoma, unclassifiable, with features intermediate between DLBCL and classic Hodgkin lymphoma 9597 Primary cutaneous follicle centre lymphoma 9650 Classical Hodgkin lymphoma 9651 Lymphocyte-rich classic Hodgkin lymphoma 9652 Mixed cellularity classic Hodgkin lymphoma 9653 Lymphocyte-depleted classic Hodgkin lymphoma 9659 Nodular lymphocyte predominant Hodgkin lymphoma 9663 Nodular sclerosis classic Hodgkin lymphoma 9673 Mantle cell lymphoma 9678 Primary effusion lymphoma 9679 Primary mediastinal (thymic) large B-cell lymphoma 9680 Diffuse large B-cell lymphoma (DLBCL) 9687 Burkitt lymphoma 9688 T-cell/histiocyte-rich large B-cell lymphoma 9689 Splenic marginal zone lymphoma 9690 Follicular lymphoma 9691 Follicular lymphoma, grade 2 9695 Follicular lymphoma, grade 1 9698 Follicular lymphoma, grade 3 9699 Extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue (MALT lymphoma) 9702 Peripheral T-cell lymphoma, NOS 9705 Angioimmunoblastic T-cell lymphoma 9708 Subcutaneous panniculitis-like T-cell lymphoma 9709 Primary cutaneous peripheral T-cell lymphomas 9712 Intravascular large B-cell lymphoma 9714 Anaplastic large cell lymphoma, ALK-positive 9715 Anaplastic large cell lymphoma, ALK-negative (2021+ only) 9716 Hepatosplenic T-cell lymphoma 9717 Enteropathy-associated T-cell lymphoma 9718 Primary cutaneous anaplastic large cell lymphoma 9719 Extranodal NK/T-cell lymphoma, nasal type 9725 Hydroa vacciniforme-like lymphoma (2018-2020 only, nonreportable as of 2021) 9726 Primary cutaneous gamma-delta T-cell lymphoma (2018-2020 only, see code 9687/3 for 2021+) 9735 Plasmablastic lymphoma 9737 ALK-positive large B-cell lymphoma 9738 HHV8-positive DLBCL, NOS 9766 Lymphomatoid granulomatosis grade 3 (2021+ only) 9826 Burkitt cell leukemia (2018-2020 only, see code 9687/3 for 2021+) 9827 Adult T-cell leukemia/lymphomaData Items
| Name | Default Value | Used in Derivation | NAACCR Item | Required By | Metadata | 
|---|---|---|---|---|---|
| Year of Diagnosis | No | NAACCR #390 dateOfDiagnosis | None | ||
| Primary Site | Yes | NAACCR #400 primarySite | None | ||
| Histology | Yes | NAACCR #522 histologicTypeIcdO3 | None | ||
| Behavior | Yes | NAACCR #523 behaviorCodeIcdO3 | None | ||
| Schema Discriminator 1 | Yes | NAACCR #3926 schemaDiscriminator1 | All | SSDI | |
| Tumor Size Clinical | 999 | No | NAACCR #752 tumorSizeClinical | None | |
| Tumor Size Pathological | 999 | No | NAACCR #754 tumorSizePathologic | None | |
| Tumor Size Summary | 999 | No | NAACCR #756 tumorSizeSummary | None | |
| Regional Nodes Positive | 99 | No | NAACCR #820 regionalNodesPositive | None | |
| Regional Nodes Examined | 99 | No | NAACCR #830 regionalNodesExamined | None | |
| LVI | 8 | No | NAACCR #1182 lymphVascularInvasion | None | |
| EOD Primary Tumor | 999 | Yes | NAACCR #772 eodPrimaryTumor | None | |
| EOD Regional Nodes | 888 | Yes | NAACCR #774 eodRegionalNodes | None | |
| EOD Mets | 88 | Yes | NAACCR #776 eodMets | None | |
| SS2018 | No | NAACCR #764 summaryStage2018 | None | ||
| Grade Clinical | 8 | No | NAACCR #3843 gradeClinical | CCCR/Canada COC NPCR SEER | SSDI | 
| Grade Pathological | 8 | No | NAACCR #3844 gradePathological | CCCR/Canada COC NPCR SEER | SSDI | 
| Grade Post Therapy Clin (yc) | No | NAACCR #1068 gradePostTherapyClin | COC NPCR SEER | SSDI | |
| Grade Post Therapy Path (yp) | No | NAACCR #3845 gradePostTherapy | CCCR/Canada COC NPCR SEER | SSDI | |
| B Symptoms | 8 | No | NAACCR #3812 bSymptoms | CCCR/Canada COC SEER | SSDI | 
| HIV Status | 8 | No | NAACCR #3859 hivStatus | COC 2018–2020 SEER | SSDI | 
| NCCN International Prognostic Index (IPI) | X8 | No | NAACCR #3896 nccnInternationalPrognosticIndex | COC SEER | SSDI | 
Initial Context
Outputs
| Name | Default Value | Description | NAACCR Item | Metadata | 
|---|---|---|---|---|
| Schema ID | 00790 | NAACCR #3800 schemaId | None | |
| Derived Version | {{ctx_alg_version}} | None | None | |
| Derived Summary Stage 2018 | 9 | NAACCR #762 derivedSummaryStage2018 | None |