Derived Summary Stage 2018: Retinoblastoma

Derived Summary Stage 2018

Default

9

NAACCR Item

NAACCR #762
SS2018 Description
1 Localized only (localized, NOS) - Confined to retina, NOS - Intraocular tumor(s) WITH local invasion, NOS + Choroid (concomitant focal invasion) + Pre- or intralaminar involvement of optic nerve head + Retinal detachment + Schlemm's canal + Stromal invasion iris + Subretinal seeding + Trabecular meshwork + Vitreous seeding - Advanced intraocular tumor(s) WITH significant local invasion + Anterior chamber + Aseptic orbital cellulitis + Buphthalmos + Choroid (multiple foci, focal, full-thickness involvement) + Ciliary body + Emissary channels + Hyphema AND/OR massive vitreous hemorrhage + Iris + Lens + Pars plana + Phthisis or pre-phthisis bulbi + Raised intraocular pressure with neovascularization + Retrolaminar invasion of optic nerve head + Sclera + Zonules
2 Regional by direct extension only - Extraocular tumor + Adjacent adipose tissue + Bone + Conjunctiva + Episclera + Extraocular muscle + Eyelids + Meningeal spaces (around optic nerve) + Optic nerve (clinical thickening) + Optic nerve (retrobulbar, extraocular) + Orbit + Orbital tissue (includes clinical orbital tissue thickening)
3 Regional lymph node(s) involved only - Cervical, NOS - Mandibular, NOS + Submandibular (submaxillary) - Parotid + Infra-auricular + Preauricular - Regional lymph node(s), NOS + Lymph node(s), NOS
4 Regional by BOTH direct extension AND regional lymph node(s) involved - Codes (2) + (3)
7 Distant site(s)/lymph node(s) involved - Distant site(s) (including further contiguous extension) + Cerebrospinal fluid + CNS parenchyma - Distant lymph node(s), NOS - Distant metastasis, NOS + Carcinomatosis + Distant metastasis WITH or WITHOUT distant lymph node(s)
9 Unknown if extension or metastasis