Summary Stage 2018: Lymphoma Ocular Adnexa
Summary Stage 2018
Notes
**Lymphoma Ocular Adnexa**
9590-9699, 9702-9719, 9725-9726, 9734-9738, 9823, 9826-9827, 9930 (C441, C690, C695-C696)
**Note 1:** **Sources used in the development of this chapter**
* SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf)
* SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/)
* Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx
* Chapter 71 *Ocular Adnexal Lymphoma*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois.
**Note 2:** **Not applicable codes**
* Code 0 is not applicable for this chapter.
**Note 3:** **Ocular adnexal lymphomas**
* Ocular adnexal lymphomas (OAL) originate in conjunctiva, eyelids, lacrimal gland, lacrimal drainage apparatus, and other orbital tissues surrounding the eye.
* This chapter should not be used for secondary lymphomatous involvement of ocular adnexa or for intraocular lymphomas.
**Note 4:** **Peripheral blood or bone marrow involvement**
* If there is peripheral blood or bone marrow involvement, code 7.
| SS2018 |
Description |
| 1 |
**Localized only (localized, NOS)**
- Lymphoma involving the conjunctiva alone WITHOUT or UNKNOWN eyelid or orbital involvement
- Lymphoma with orbital involvement WITH or WITHOUT conjunctival involvement
- Lymphoma with preseptal eyelid involvement WITH or WITHOUT orbital or conjunctival involvement |
| 2 |
**Regional by direct extension only**
- Orbital adnexal lymphoma AND extraorbital lymphoma extending beyond the orbit to adjacent structures
+ Bone
+ Brain
+ Maxillofacial sinuses |
| 3 |
**Regional lymph node(s) involved only**
- Cervical
- Parotid
- Preauricular
- Regions draining the ocular adnexal structures
- Submandibular
- Regional lymph node(s), NOS
+ Lymph node(s), NOS |
| 4 |
**Regional by BOTH direct extension AND regional lymph node(s) involved**
Codes (2) + (3) |
| 7 |
**Distant site(s)/lymph node(s) involved**
- Distant sites
+ Non-contiguous involvement of other extranodal sites including, but not limited to
* Breast
* Gastrointestinal tract
* Kidney
* Liver
* Lung
* Parotid gland
* Salivary gland
* Spleen
* Submandibular gland
- Distant lymph node(s), NOS
+ Diffuse OR disseminated involvement of peripheral and central lymph node regions
+ Mediastinum
- Distant metastasis, NOS
+ Blood/peripheral blood
+ Bone marrow
+ Distant metastasis WITH or WITHOUT distant lymph node(s) |
| 9 |
Unknown if extension or metastasis |
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998
(2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001.
(3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL)
(4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017
(5) Heegaard, S., Finger, P.T., et al. **Ocular Adnexal Lymphoma**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017
