Summary Stage 2018: Lymphoma Ocular Adnexa

Summary Stage 2018

Notes

**Lymphoma Ocular Adnexa** 9590-9699, 9702-9719, 9725-9726, 9734-9738, 9823, 9826-9827, 9930 (C441, C690, C695-C696) **Note 1:** **Sources used in the development of this chapter** * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 71 *Ocular Adnexal Lymphoma*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** **Not applicable codes** * Code 0 is not applicable for this chapter. **Note 3:** **Ocular adnexal lymphomas** * Ocular adnexal lymphomas (OAL) originate in conjunctiva, eyelids, lacrimal gland, lacrimal drainage apparatus, and other orbital tissues surrounding the eye. * This chapter should not be used for secondary lymphomatous involvement of ocular adnexa or for intraocular lymphomas. **Note 4:** **Peripheral blood or bone marrow involvement** * If there is peripheral blood or bone marrow involvement, code 7.

NAACCR Item

NAACCR #764
SS2018 Description
1 **Localized only (localized, NOS)** - Lymphoma involving the conjunctiva alone WITHOUT or UNKNOWN eyelid or orbital involvement - Lymphoma with orbital involvement WITH or WITHOUT conjunctival involvement - Lymphoma with preseptal eyelid involvement WITH or WITHOUT orbital or conjunctival involvement
2 **Regional by direct extension only** - Orbital adnexal lymphoma AND extraorbital lymphoma extending beyond the orbit to adjacent structures + Bone + Brain + Maxillofacial sinuses
3 **Regional lymph node(s) involved only** - Cervical - Parotid - Preauricular - Regions draining the ocular adnexal structures - Submandibular - Regional lymph node(s), NOS + Lymph node(s), NOS
4 **Regional by BOTH direct extension AND regional lymph node(s) involved** Codes (2) + (3)
7 **Distant site(s)/lymph node(s) involved** - Distant sites + Non-contiguous involvement of other extranodal sites including, but not limited to * Breast * Gastrointestinal tract * Kidney * Liver * Lung * Parotid gland * Salivary gland * Spleen * Submandibular gland - Distant lymph node(s), NOS + Diffuse OR disseminated involvement of peripheral and central lymph node regions + Mediastinum - Distant metastasis, NOS + Blood/peripheral blood + Bone marrow + Distant metastasis WITH or WITHOUT distant lymph node(s)
9 Unknown if extension or metastasis
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998 (2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001. (3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL) (4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017 (5) Heegaard, S., Finger, P.T., et al. **Ocular Adnexal Lymphoma**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017