Summary Stage 2018: Kaposi Sarcoma

Summary Stage 2018

Notes

**Kaposi Sarcoma** 9140 Kaposi Sarcoma (C000-C699, C739-C750, C754-C809) **Note 1:** The following sources were used in the development of this chapter * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 45 *Soft Tissue Sarcoma - Unusual Histologies and Sites*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** Kaposi Sarcoma of the brain, central nervous system and intracranial glands is now collected in the following: * C700, C710-C719: Brain * C701, C709, C720-C725, C728-C729: CNS Other * C751-C753: Intracranial Gland **Note 3:** Summary Stage is the only applicable staging system for this site/histology/schema. **Note 4:** Code 0 is not applicable for this chapter.

NAACCR Item

NAACCR #764
SS2018 Description
1 Localized only - Single or multiple lesion(s) + Mucosa (e.g., oral cavity, anus, rectum, vagina, vulva) + Skin and/or connective tissue + Viscera (e.g., pulmonary, gastrointestinal tract, spleen, other)
2 Regional by direct extension only - Multiple lesion(s) + Mucosa plus skin and/or connective tissue + Viscera plus mucosa + Viscera plus skin and/or connective tissue
3 Regional lymph node(s) involved only - Both clinically enlarged palpable lymph node(s) (adenopathy) and pathologically positive lymph node(s) - Clinically enlarged palpable lymph node(s) (adenopathy) and either pathologically negative node(s) or no pathological statement - No clinically enlarged palpable lymph node(s) (adenopathy) but pathologically positive lymph node(s) - Regional lymph node(s), NOS + Lymph node(s), NOS
4 Regional by BOTH direct extension AND regional lymph node(s) involved - Codes (2) + (3)
7 Distant site(s)/lymph node(s) involved - Distant site(s) (including further contiguous extension) + Multiple lesions in all THREE of following: viscera plus mucosa plus skin and/or connective tissue - Distant lymph node(s), NOS - Distant metastasis, NOS + Carcinomatosis + Distant metastasis WITH or WITHOUT distant lymph node(s)
9 Unknown if extension or metastasis
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998 (2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions,** National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001. (3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05.** American Joint Committee on Cancer (Chicago, IL) (4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017 (5) Pollock, R.E., Maki, R.G. **Introduction to Soft Tissue Sarcoma** In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017 (6) Maki, R.G., Pollock, R.E., et al. **Soft Tissue Sarcoma - Unusual Histologies and Sites**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 539-545