Summary Stage 2018: Primary Cutaneous Lymphomas (excluding MF and SS)
Summary Stage 2018
Notes
**Primary Cutaneous Lymphomas (excluding MF and SS)**
9597, 9680, 9708-9709, 9712, 9718-9719, 9726
C440, C442-C449, C510, C609, C632
C440 Skin of lip, NOS
C442 External ear
C443 Skin of other and unspecified parts of face
C444 Skin of scalp and neck
C445 Skin of trunk
C446 Skin of upper limb and shoulder
C447 Skin of lower limb and hip
C448 Overlapping lesion of skin
C449 Skin, NOS
C510 Labium majus
C609 Penis
C632 Scrotum, NOS
**Note 1:** The following sources were used in the development of this chapter
* SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf)
* SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/ssm2000/)
* Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx
* Chapter 81 *Primary Cutaneous Lymphomas*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois.
**Note 2:** Code 0 is not applicable for this chapter.
**Note 3:** See the *Mycosis Fungoides* chapter for Mycosis Fungoides (9700) and Sezary syndrome (9701).
**Note 4:** Chapter includes the preferred terms based on the 2017 *WHO Classification of Haematopoietic and Lymphoid Tissues*
9597 Primary cutaneous follicle center lymphoma
9680 Primary cutaneous diffuse large B-cell lymphoma, leg type
9708 Subcutaneous panniculitis-like T-cell lymphoma
9709 Primary cutaneous peripheral T-cell lymphomas
9712 Intravascular large B-cell lymphoma
9718 Primary cutaneous anaplastic large cell lymphoma
9719 Extranodal NK/T-cell lymphoma, nasal type
9726 Primary cutaneous gamma-delta t-cell lymphoma
| SS2018 |
Description |
| 1 |
Localized only
- Solitary lesion
- Solitary skin involvement |
| 2 |
Regional by direct extension only
- Multiple lesions confined to one or two contiguous body regions
- Multiple lesions, NOS
- Regional skin involvement |
| 3 |
Regional lymph node(s) involved only
- Cenrowal
- Peripheral node region that drains an area of current or prior skin involvement
- Regional lymph node(s), NOS
+ Lymph node(s), NOS |
| 4 |
Regional by BOTH direct extension AND regional lymph node(s) involved
- Codes (2) + (3) |
| 7 |
Distant site(s)/lymph node(s) involved
- Distant site(s) (including further contiguous extension)
+ Extracutaneous non-lymph node disease present
+ Generalized skin involvement
+ Multiple lesions confined to discontiguous body regions
+ Multiple lesions confined to three or more contiguous body regions
+ Visceral (non-cutaneous) metastasis
- Distant lymph node(s), NOS
- Distant metastasis, NOS
+ Carcinomatosis
+ Distant metastasis WITH or WITHOUT distant lymph node(s) |
| 9 |
Unknown if extension or metastasis |
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998
(2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001.
(3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL)
(4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 3-30
(5) **Introduction to Hematologic Malignancies**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 931-935
(6) Rosen, S.T., Jaffe, E.S., Leonard, J.P., et al. **Primary Cutaneous Lymphomas**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 967-972
