Summary Stage 2018: Vulva
Summary Stage 2018
Notes
**Vulva**
8000-8040, 8042-8180, 8191-8246, 8248-8700, 9020, 9071
C510-C512, C518-C519
C510 Labium majus
C511 Labium minus
C512 Clitoris
C518 Overlapping lesion of vulva
C519 Vulva, NOS
**Note 1:** The following sources were used in the development of this chapter
* SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf)
* SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/)
* Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx
* Chapter 50 *Vulva*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois.
**Note 2:** See the following chapters for the listed histologies
* 8041, 8190, 8247: *Merkel Cell Skin*
* 88710-8714, 8800-8934, 8940-9016, 9030-9070, 9072-9137, 9141-9582: *Soft Tissue*
* 8720-8790: *Melanoma Skin*
* 8935-8936: *GIST*
* 9140: *Kaposi Sarcoma*
* 9700-9701: *Mycosis Fungoides*
**Note 3:** Basal and squamous cell carcinomas of the skin of the vulva are coded to C519 and are reportable; basal and squamous carcinomas of the skin of the perineum would be coded to C445 and would not be reportable.
| SS2018 |
Description |
| 0 |
In situ: noninvasive, intraepithelial |
| 1 |
Localized only (localized, NOS)
- FIGO Stage IA, IB, I [NOS]
+ Invasive carcinoma WITH or WITHOUT stromal invasion confined to
* Musculature
* Submucosa
* Vulva including skin |
| 2 |
Regional by direct extension only
- FIGO Stage II
+ Adjacent perineal structures
+ Anus
+ Bladder wall or bladder, NOS excluding mucosa
+ Perianal skin
+ Rectal wall or rectum, NOS excluding mucosa
+ Urethra, NOS
* Lower/distal third of urethra
+ Vagina, NOS
+ Vulva and perineum involved WITH or WITHOUT stromal invasion |
| 3 |
Regional lymph node(s) involved only
- FIGO Stage IIIA, IIIB, IIIC, III [NOS]
+ Deep inguinal, NOS
+ Femoral
+ Inguinal, NOS
+ Inguinofemoral (groin)
+ Node of Cloquet or Rosenmuller (highest deep inguinal)
+ Superficial inguinal (femoral)
+ Regional lymph node(s), NOS
* Lymph node(s), NOS
- FIGO Stage IVA based on regional lymph node involvement |
| 4 |
Regional by BOTH direct extension AND regional lymph node(s) involved
- Codes (2) + (3) |
| 7 |
Distant site(s)/lymph node(s) involved
- Distant site(s) (including further contiguous extension)
+ FIGO Stage IVA, IVB, IV [NOS]
* Bladder mucosa
* Fixed to pubic bone (pelvic bone)
* Perineal body
* Rectal mucosa
* Urethra: upper/proximal two-thirds
- Distant lymph node(s), NOS
+ Common iliac
+ External iliac
+ Internal iliac (hypogastric)
+ Obturator
+ Pelvic, NOS
- Distant metastasis, NOS
+ Carcinomatosis
+ Distant metastasis WITH or WITHOUT distant lymph node(s) |
| 9 |
Unknown if extension or metastasis |
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998
(2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001.
(3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL)
(4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 3-30
(5) **Introduction to Female Reproductive Organs**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 631
(6) Gibb, R.K., Olawaiye, A.B., Mutch, D.G., et al. **Vulva**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 633-640
