EOD Primary Tumor

This input is used for staging

Notes

**Note:** This is a new schema for pheochromocytomas (PHs) and paragangliomas (PGs), which are rare neuroendocrine tumors originating in the paraganglia. Pheochromocytomas originate in the adrenal medulla and sympathetic tumors. Paragangliomas originate either in the parasympathetic or sympathetic autonomous nervous system ganglia, which is outside the adrenal medulla.

Default

999

NAACCR Item

NAACCR #772

Code	Description	SS2018 T
000	In situ: Noninvasive; intraepithelial	IS
100	Any size pheochromocytoma (PH) tumor, no extra-adrenal invasion Confined to adrenal gland Localized, NOS	L
200	Any size paraganglioma (PG) tumor, no extra-adrenal invasion	L
300	Adjacent connective tissue Gerota’s fascia Invasion of adjacent organs - Blood vessels (large) + Renal vein + Vena cava - Kidney - Retroperitoneal structures including + Great vessels * Aorta * Inferior vena cava	RE
700	Diaphragm Liver Pancreas Spleen Further contiguous extension	D
800	No evidence of primary tumor	U
999	Unknown; extension not stated Primary tumor cannot be assessed Not documented in patient record Death Certificate Only	U

1. Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998 2. Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions,** National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001. 3. Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05.** American Joint Committee on Cancer (Chicago, IL) 4. Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 3-30 5. Jimenez, C., Perrier, N.D., et al. **Adrenal – Neuroendocrine Tumors**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 919-927