Summary Stage 2018: Mycosis Fungoides
Summary Stage 2018
Notes
**Mycosis Fungoides**
9700-9701 (C000-C002, C006, C440-C449, C510-C512, C518-C519, C600-C602, C608-C609, C632)
**Note 1:** The following sources were used in the development of this chapter
* SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf)
* SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/)
* Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx
* Chapter 81 *Primary Cutaneous Lymphomas*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois.
**Note 2:** For mycosis fungoides of sites other than those above, use the appropriate site-specific schema.
**Note 3:** Code 0 is not applicable for this chapter.
**Note 4:** All lymph node (regional and distant) involvement is coded as regional lymph node involvement.
**Note 5:** Visceral involvement is metastatic disease and should be questioned in the absence of node or blood involvement.
| SS2018 |
Description |
| 1 |
Localized only (localized, NOS)
- MFCG Stage I
+ Less than 10% of skin surface, no tumors
+ Limited to patches, papules, or plaques
- MFCG Stage II
+ Greater than or equal to 10% of skin surface, no tumors
+ Generalized patches, papules, or plaques
- Not stated whether patches, papules, or plaques
+ % of body surface not stated, no tumors
+ Skin involvement, NOS: extent not stated, no tumors |
| 2 |
Regional by direct extension only
- MFCG Stage III
+ Cutaneous tumor, size not stated
+ Generalized erythroderma (confluence of erythemia)
* (greater than 50% of body involved with diffuse redness)
+ One or more tumors equal to 1 cm or greater
+ Sezary syndrome
+ Skin lesion described as tumor less than 1 cm |
| 3 |
Regional lymph node(s) involved only
- Both clinically enlarged palpable lymph node(s) (adenopathy) AND
+ pathologically positive nodes
- Clinically enlarged palpable lymph node(s) (adenopathy) AND
+ either pathologically negative nodes or no pathological statement
- No clinically enlarged palpable lymph node(s) (adenopathy) BUT
+ pathologically positive lymph node(s)
- Dutch grade 1-4 OR NCI LN 0-4
+ Clone positive, negative or unknown
- Regional lymph node(s), NOS
+ Lymph node(s), NOS |
| 4 |
Regional by BOTH direct extension AND regional lymph node(s) involved
- Codes (2) + (3) |
| 7 |
Distant site(s) involved
- Distant site(s) (including further contiguous extension)
+ MFCG Stage IV
* Bone marrow
* Involvement by at least one organ outside the skin, nodes, blood, or bone marrow
* Liver
* Spleen
* Visceral (non-cutaneous, extranodal) involvement, pathologically confirmed
- Distant metastasis, NOS
+ Carcinomatosis |
| 9 |
Unknown if extension or metastasis |
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998
(2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001.
(3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL)
(4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 3-30
(5) **Introduction to Hematologic Malignancies**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 931-935
(6) Rosen, S.T., Jaffe, E.S., Leonard, J.P., et al. **Primary Cutaneous Lymphomas**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 967-972
