Summary Stage 2018: Vulva

Summary Stage 2018

Notes

**Vulva** C510 Labium majus C511 Labium minus C512 Clitoris C518 Overlapping lesion of vulva C519 Vulva, NOS **Note 1:** The following sources were used in the development of this schema * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 50 *Vulva*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** See the following schemas for the listed histologies * 8247 Merkel Cell Skin * 8720-8790 Melanoma Skin * 9140 Kaposi Sarcoma * 9700-9701 Mycosis Fungoides **Note 3:** Basal and squamous cell carcinomas of the skin of the vulva are coded to C519 and are reportable; basal and squamous carcinomas of the skin of the perineum would be coded to C445 and would not be reportable.

NAACCR Item

NAACCR #764
SS2018 Description
0 In situ: noninvasive, intraepithelial
1 Localized only (localized, NOS) - FIGO Stage IA, IB, I [NOS] + Invasive carcinoma WITH or WITHOUT stromal invasion confined to * Musculature * Submucosa * Vulva including skin
2 Regional by direct extension only - FIGO Stage II + Adjacent perineal structures + Anus + Bladder wall or bladder, NOS excluding mucosa + Perianal skin + Rectal wall or rectum, NOS excluding mucosa + Urethra, NOS * Lower/distal third of urethra + Vagina, NOS + Vulva and perineum involved WITH or WITHOUT stromal invasion
3 Regional lymph node(s) involved only - FIGO Stage IIIA, IIIB, IIIC, III [NOS] + Deep inguinal, NOS + Femoral + Inguinal, NOS + Inguinofemoral (groin) + Node of Cloquet or Rosenmuller (highest deep inguinal) + Superficial inguinal (femoral) + Regional lymph node(s), NOS * Lymph node(s), NOS - FIGO Stage IVA based on regional lymph node involvement
4 Regional by BOTH direct extension AND regional lymph node(s) involved - Codes (2) + (3)
7 Distant site(s)/lymph node(s) involved - Distant site(s) (including further contiguous extension) + FIGO Stage IVA, IVB, IV [NOS] * Bladder mucosa * Fixed to pubic bone (pelvic bone) * Perineal body * Rectal mucosa * Urethra: upper/proximal two-thirds - Distant lymph node(s), NOS + Common iliac + External iliac + Internal iliac (hypogastric) + Obturator + Pelvic, NOS - Distant metastasis, NOS + Carcinomatosis + Distant metastasis WITH or WITHOUT distant lymph node(s)
9 Unknown if extension or metastasis
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998 (2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001. (3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL) (4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 3-30 (5) **Introduction to Female Reproductive Organs**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 631 (6) Gibb, R.K., Olawaiye, A.B., Mutch, D.G., et al. **Vulva**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 633-640