Summary Stage 2018: Orbital Sarcoma

Summary Stage 2018

Notes

**Orbit** C690-C696, C698, C699, C723 C690 Conjunctiva C691 Cornea, NOS C692 Retina C693 Choroid C694 Ciliary Body C695 Lacrimal Gland C696 Orbit, NOS C698 Overlapping lesion of eye and adnexa C699 Eye, NOS C723 Optic nerve **Note 1:** The following sources were used in the development of this schema * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 70 *Orbital Sarcoma*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** Code 0 is not applicable for this schema

NAACCR Item

NAACCR #764
SS2018 Description
1 Localized only (localized, NOS) - Confined to orbit (including soft tissues)
2 Regional by direct extension only - Adjacent paranasal sinuses - Bony walls - Conjunctiva - Cranium - Diffuse invasion of orbital tissue and bony walls - Globe - Orbital tissues (excluding orbit primary site) - Periorbital structures
3 Regional lymph node(s) involved only - Cervical, NOS - Mandibular, NOS + Submandibular (submaxillary) - Parotid, NOS + Infra-auricular + Preauricular - Regional lymph node(s), NOS + Lymph node(s), NOS
4 Regional by BOTH direct extension AND regional lymph node(s) involved - Codes (2) + (3)
7 Distant site(s)/lymph node(s) involved - Distant site(s) (including further contiguous extension) + Central nervous system + Eyelid(s) + Nasal cavity + Temporal fossa - Distant lymph node(s), NOS - Distant metastasis, NOS + Carcinomatosis + Distant metastasis WITH or WITHOUT distant lymph node(s)
9 Unknown if extension or metastasis
(1) Fritz AG, Ries LAG (eds). **SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998)**, National Cancer Institute, NIH Pub. No. 98-2313, Bethesda, MD, 1998 (2) Young JL Jr, Roffers SD, Ries LAG, Fritz AG, Hurlbut AA (eds.). **SEER Summary Staging Manual-2000: Codes and Coding Instructions**, National Cancer Institute, NIH Pub. No. 01-4969, Bethesda, MD, 2001. (3) Collaborative Stage Work Group of the American Joint Committee on Cancer. **Collaborative Stage Data Collection System User Documentation and Coding Instructions, version 02.05**. American Joint Committee on Cancer (Chicago, IL) (4) Gress, D.M., Edge, S.B., Gershenwald, J.E., et al. **Principles of Cancer Staging**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 3-30 (5) Dutton, J.J., Finger, P.T., et al. **Orbital Sarcoma**. In: Amin, M.B., Edge, S.B., Greene, F.L., et al. (Eds.) AJCC Cancer Staging Manual. 8th Ed. New York: Springer; 2017: 841-848