Summary Stage 2018: Mycosis Fungoides
Summary Stage 2018
Notes
**Mycosis Fungoides** C000 Vermilion border of upper lip (excludes external upper lip) C001 Vermilion border of lower lip (excludes external lower lip) C002 Vermilion border of lip, NOS (excludes external lip, NOS) C006 Commissure of lip C440 Skin of lip, NOS C441 Skin of eyelid C442 External ear C443 Skin of other and unspecified parts of face C444 Skin of scalp and neck C445 Skin of trunk C446 Skin of upper limb and shoulder C447 Skin of lower limb and hip C448 Overlapping lesion of skin C449 Skin, NOS C510 Labium majus C511 Labium minus C512 Clitoris C518 Overlapping lesion of vulva C519 Vulva, NOS C600 Prepuce C601 Glans penis C602 Body of penis C608 Overlapping lesion of penis C609 Penis C632 Scrotum, NOS **Note 1:** The following sources were used in the development of this schema * SEER Extent of Disease 1988: Codes and Coding Instructions (3rd Edition, 1998) (https://seer.cancer.gov/archive/manuals/EOD10Dig.3rd.pdf) * SEER Summary Staging Manual-2000: Codes and Coding Instructions (https://seer.cancer.gov/tools/ssm/) * Collaborative Stage Data Collection System, version 02.05: https://cancerstaging.org/cstage/Pages/default.aspx * Chapter 81 *Primary Cutaneous Lymphomas*, in the AJCC Cancer Staging Manual, Eighth Edition (2017) published by Springer International Publishing. Used with permission of the American College of Surgeons, Chicago, Illinois. **Note 2:** Code 0 is not applicable for this schema. **Note 3:** All lymph node (regional and distant) involvement is coded as regional lymph node involvement. **Note 4:** Visceral involvement is metastatic disease and should be questioned in the absence of node or blood involvement.NAACCR Item
NAACCR #764| SS2018 | Description |
|---|---|
| 1 | Localized only (localized, NOS) - MFCG Stage I + Less than 10% of skin surface, no tumors + Limited to patches, papules, or plaques - MFCG Stage II + Greater than or equal to 10% of skin surface, no tumors + Generalized patches, papules, or plaques - Not stated whether patches, papules, or plaques + % of body surface not stated, no tumors + Skin involvement, NOS: extent not stated, no tumors |
| 2 | Regional by direct extension only - MFCG Stage III + Cutaneous tumor, size not stated + Generalized erythroderma (confluence of erythemia) * (greater than 50% of body involved with diffuse redness) + One or more tumors equal to 1 cm or greater + Sezary syndrome + Skin lesion described as tumor less than 1 cm |
| 3 | Regional lymph node(s) involved only - Both clinically enlarged palpable lymph node(s) (adenopathy) AND + pathologically positive nodes - Clinically enlarged palpable lymph node(s) (adenopathy) AND + either pathologically negative nodes or no pathological statement - No clinically enlarged palpable lymph node(s) (adenopathy) BUT + pathologically positive lymph node(s) - Dutch grade 1-4 OR NCI LN 0-4 + Clone positive, negative or unknown - Regional lymph node(s), NOS + Lymph node(s), NOS |
| 4 | Regional by BOTH direct extension AND regional lymph node(s) involved - Codes (2) + (3) |
| 7 | Distant site(s) involved - Distant site(s) (including further contiguous extension) + MFCG Stage IV * Bone marrow * Involvement by at least one organ outside the skin, nodes, blood, or bone marrow * Liver * Spleen * Visceral (non-cutaneous, extranodal) involvement, pathologically confirmed - Distant metastasis, NOS + Carcinomatosis |
| 9 | Unknown if extension or metastasis |